| Db | Link | Name | Definition | Comment | Is a |
|---|---|---|---|---|---|
| OMIM | OMIM:106400 | ANKYLOSING VERTEBRAL HYPEROSTOSIS WITH TYLOSIS | — | — | — |
| OMIM | OMIM:106500 | ANNULAR ERYTHEMA | — | — | — |
| OMIM | OMIM:106600 | TOOTH AGENESIS, SELECTIVE, 1; STHAG1 | — | — | — |
| OMIM | OMIM:106700 | TOTAL ANOMALOUS PULMONARY VENOUS RETURN 1; TAPVR1 | — | — | — |
| OMIM | OMIM:106750 | ANONYCHIA WITH FLEXURAL PIGMENTATION | — | — | — |
| OMIM | OMIM:106900 | ANONYCHIA-ECTRODACTYLY | — | — | — |
| OMIM | OMIM:106990 | ANONYCHIA-ONYCHODYSTROPHY WITH BRACHYDACTYLY TYPE B AND ECTRODACTYLY | — | — | — |
| OMIM | OMIM:106995 | ANONYCHIA-ONYCHODYSTROPHY WITH HYPOPLASIA OR ABSENCE OF DISTAL PHALANGES | — | — | — |
| OMIM | OMIM:107000 | NAIL DISORDER, NONSYNDROMIC CONGENITAL, 6; NDNC6 | — | — | — |
| OMIM | OMIM:107100 | ANORECTAL ANOMALIES | — | — | — |
| OMIM | OMIM:107200 | ANOSMIA, ISOLATED CONGENITAL; ANIC | — | — | — |
| OMIM | OMIM:107240 | MOVED TO 116930 | — | — | — |
| OMIM | OMIM:107250 | ANTERIOR SEGMENT DYSGENESIS 1; ASGD1 | — | — | — |
| OMIM | OMIM:107253 | REMOVED FROM DATABASE | — | — | — |
| OMIM | OMIM:107290 | ANTIPYRINE METABOLISM | — | — | — |
| OMIM | OMIM:107320 | ANTIPHOSPHOLIPID SYNDROME, FAMILIAL | — | — | — |
| OMIM | OMIM:107410 | SERPIN PEPTIDASE INHIBITOR, CLADE A, MEMBER 2, PSEUDOGENE; SERPINA2P | — | — | — |
| OMIM | OMIM:107440 | ANTIVIRAL STATE REPRESSOR, REGULATOR OF; AVRR | — | — | — |
| OMIM | OMIM:107460 | MOVED TO 107450 | — | — | — |
| OMIM | OMIM:107480 | TOWNES-BROCKS SYNDROME 1; TBS1 | — | — | — |
| OMIM | OMIM:107500 | AORTIC ARCH ANOMALY WITH PECULIAR FACIES AND MENTAL RETARDATION | — | — | — |
| OMIM | OMIM:107550 | AORTIC ARCH INTERRUPTION, FACIAL PALSY, AND RETINAL COLOBOMA | — | — | — |
| OMIM | OMIM:107600 | APLASIA CUTIS CONGENITA, NONSYNDROMIC; ACC | — | — | — |
| OMIM | OMIM:107601 | MOVED TO 100300 | — | — | — |
| OMIM | OMIM:107640 | APNEA, CENTRAL SLEEP | — | — | — |