| Db | Link | Name | Definition | Comment | Is a |
|---|---|---|---|---|---|
| OMIM | OMIM:105565 | ANAL SPHINCTER MYOPATHY, INTERNAL | — | — | — |
| OMIM | OMIM:105570 | ANDROSTENONE, ABILITY TO SMELL | — | — | — |
| OMIM | OMIM:105580 | ANAL CANAL CARCINOMA | — | — | — |
| OMIM | OMIM:105600 | ANEMIA, CONGENITAL DYSERYTHROPOIETIC, TYPE III; CDAN3 | — | — | — |
| OMIM | OMIM:105650 | DIAMOND-BLACKFAN ANEMIA 1; DBA1 | — | — | — |
| OMIM | OMIM:105800 | ANEURYSM, INTRACRANIAL BERRY, 1; ANIB1 | — | — | — |
| OMIM | OMIM:105805 | ANEURYSM OF INTERVENTRICULAR SEPTUM | — | — | — |
| OMIM | OMIM:105830 | ANGELMAN SYNDROME; AS | — | — | — |
| OMIM | OMIM:105835 | ANGEL-SHAPED PHALANGOEPIPHYSEAL DYSPLASIA; ASPED | — | — | — |
| OMIM | OMIM:106050 | ANGIOMA SERPIGINOSUM, AUTOSOMAL DOMINANT | — | — | — |
| OMIM | OMIM:106070 | ANGIOMA, HEREDITARY NEUROCUTANEOUS | — | — | — |
| OMIM | OMIM:106100 | ANGIOEDEMA, HEREDITARY, TYPE I; HAE1 | — | — | — |
| OMIM | OMIM:106150 | ANGIOTENSINOGEN; AGT | — | — | — |
| OMIM | OMIM:106160 | MOVED TO 106165 | — | — | — |
| OMIM | OMIM:106180 | ANGIOTENSIN I-CONVERTING ENZYME; ACE | — | — | — |
| OMIM | OMIM:106190 | ANHIDROSIS, ISOLATED, WITH NORMAL SWEAT GLANDS; ANHD | — | — | — |
| OMIM | OMIM:106200 | MOVED TO 106210 | — | — | — |
| OMIM | OMIM:106210 | ANIRIDIA 1; AN1 | — | — | — |
| OMIM | OMIM:106220 | ANIRIDIA AND ABSENT PATELLA | — | — | — |
| OMIM | OMIM:106230 | ANIRIDIA, MICROCORNEA, AND SPONTANEOUSLY REABSORBED CATARACT | — | — | — |
| OMIM | OMIM:106240 | ANISOCORIA | — | — | — |
| OMIM | OMIM:106250 | ANKYLOBLEPHARON FILIFORME ADNATUM AND CLEFT PALATE; AFA | — | — | — |
| OMIM | OMIM:106260 | ANKYLOBLEPHARON-ECTODERMAL DEFECTS-CLEFT LIP/PALATE | — | — | — |
| OMIM | OMIM:106280 | ANKYLOGLOSSIA | — | — | — |
| OMIM | OMIM:106300 | SPONDYLOARTHROPATHY, SUSCEPTIBILITY TO, 1; SPDA1 | — | — | — |